Keywords
Inflammatory disease
Vasculitis
Aortitis
Categories
How to Cite
Abstract
Cogan's syndrome is a rare inflammatory pathology that usually presents with ocular and vestibulocochlear symptoms, but in a low percentage of patients it can be associated with systemic manifestations vasculitis-like. The treatment of this syndrome is not clear and is based on immunosuppressive regimens similar to those of other autoimmune diseases. When it presents with severe manifestations such as acute coronary syndrome with a possible indication for surgery, best time for the invasive procedure is unkown. We present the case of a patient with Cogan's syndrome and aortitis that caused significant extrinsic compression of the left main coronary artery, as well as its evolution, treatment, and review of the currently available literature.References
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Copyright (c) 2024 Lucas Barros López, Jessica Giménez Lecina, Mónica Requesens Solera, Sara Noblejas Drouot, María Barrera Sánchez , José Javier Muñoz Marco